Subacute compressive myelopathy secondary to extramedullary hematopoiesis.

نویسندگان

  • Paulo Victor Sgobbi de Souza
  • Wladimir Bocca Vieira de Rezende Pinto
  • José Luiz Pedroso
  • Orlando Graziani Povoas Barsottini
چکیده

A 25-year-old man presented with subacute onset paraparesis with sphincter disturbance. His past medical history unvealed b-thalassemia intermedia (compound heterozygote IVS 1-5) and hereditary persistence of fetal hemoglobin type 2. His neurological examination disclosed a complete spinal cord syndrome without clear thoracic sensory level. Spinal cord imaging showed severe thoracic spinal stenosis secondary to paraspinal extramedullary hematopoiesis (Figure). Spinal cord compression is a leading cause of myelopathy in patients with multiple progressive paravertebral masses in chronic extramedullary hematopoiesis, described in hereditary hemoglobinopathies, lymphoproliferative disorders, myelofibrosis and polycythemia vera.

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عنوان ژورنال:
  • Arquivos de neuro-psiquiatria

دوره 72 9  شماره 

صفحات  -

تاریخ انتشار 2014